Enzyme:

Enzyme Properties

EntryP36551 Entry NameHEM6_HUMAN
Protein NamesOxygen-dependent coproporphyrinogen-III oxidase, mitochondrial (COX) (Coprogen oxidase) (Coproporphyrinogenase) (EC 1.3.3.3)
Gene NamesCPOX CPO CPX OrganismHomo sapiens (Human)
EC NumbersEC 1.3.3.3 Enzyme TypeOxidoreductases
Length454.0 aa Reviewed Reviewed
From SourceP36551

Associated Reactions

Reaction ID: AKRT014833

Reaction: Cc1c2[nH]c(c1CCC(=O)O)Cc1[nH]c(c(CCC(=O)O)c1C)Cc1[nH]c(c(CCC(=O)O)c1C)Cc1[nH]c(c(C)c1CCC(=O)O)C2 → O=C=O

Substrate
Product
Source Link: RXN0-1461
Reaction ID: AKRT014831

Reaction: Cc1c2[nH]c(c1CCC(=O)O)Cc1[nH]c(c(CCC(=O)O)c1C)Cc1[nH]c(c(CCC(=O)O)c1C)Cc1[nH]c(c(C)c1CCC(=O)O)C2 → C=Cc1c2[nH]c(c1C)Cc1[nH]c(c(CCC(=O)O)c1C)Cc1[nH]c(c(C)c1CCC(=O)O)Cc1[nH]c(c(C)c1C=C)C2

Substrate
Product
Source Link: RXN0-1461